A.脊髓前角α-運(yùn)動(dòng)神經(jīng)元缺失以及神經(jīng)膠質(zhì)細(xì)胞增生 B.腦干疑核、舌下神經(jīng)核和面神經(jīng)核神經(jīng)元減少,殘存神經(jīng)元?dú)馇驑幼?br /> C.肌肉活檢可見(jiàn)大量萎縮的Ⅰ型肌纖維 D.電鏡下可見(jiàn)肌纖維萎縮、肌小節(jié)排列紊亂、神經(jīng)纖維稀疏和軸索萎縮等